19 Biliary Disorders

Biliary Atresia

  • closed/absent bile duct

Primary Biliary Cirrhosis

  • without obstruction/mass/stones
  • obstruction inside liver

  • no jaundice/RUQ pain

  • itching and very high alk phos

  • can't get lipids out in bile
  • RUQ US: nl bile duct

  • ultimately cirrhosis

Primary Sclerosing Cholangitis

  • biliary tree stuck together. Bile can't flow
  • primary biliary cirrhosis only intra ducts
  • complication of ulcerative colitis

  • scar, fibers form as result of inflammation, then strictures form

Diagnosis

  • fibrous tissues laid down in circles around ducts

  • beads on a string

Treatment

  • cholangiocarcinoma risk

Cholangiocarcinoma