Interstitial pneumonia with autoimmune features challenges and controversies
Persistent Notes
Highlights
- interstitial pneumonia with autoimmune features p.1
- Connective tissue diseases p.1
- ILD in the presence of features suggestive of, but not confirmatory for, p.1
- a define p.1
- CTD. p.1
- idiopathic interstitial pneumonia p.2
- n overlap between IIPs and CTD-ILD p.2
- overlap CTD p.2
- h features of separate CTD p.2
- are present in the same patient p.2
- exposed to inhaled antigens p.2
- with some IPAF series being “close t p.3
- IPF cases” and others “closer to CTD-ILD cases”. p.3
- h abnormal nailfold capillaroscopy p.4
- salivary gland biopsy, p.4
- inclusion of selected additional items p.4
- sicca symptoms p.4
- Myositis-specific antibodies p.4
- anti-synthetase antibodies p.4
- IPAF patients with MSA p.7
- were more frequently characterised by a computed tomography p.7
- non-specific interstitial pneumonia p.7
- ) Interstitial pneumonia with autoimmune features p.8
- Positive serology for anti-OJ p.8
- (ANA) p.8
- rheumatoid factor p.8
- a UIP pattern. p.8
- non-UIP histological pattern p.9
- “multi-compartment involvement”, p.9
- treatment of gastro-oesophageal reflux i p.13
- glucocorticoids p.14
- immunosuppressive therapy p.14
- cyclophosphamide, followed by maintenance mycophenolate and prednisolone p.14
- mycophenolate p.14
- Nintedanib p.15
- (the INBUILD study) p.15
- SENSCIS p.15
- e observation without dru p.15
- therapy, immunomodulation with glucocorticoids and/or immunosuppressants, antifibrotic drugs, a p.15
Reference
Mackintosh JA, Wells AU, Cottin V, Nicholson AG, Renzoni EA. Interstitial pneumonia with autoimmune features: challenges and controversies. Eur Respir Rev. 2021;30(162):210177. doi:10.1183/16000617.0177-2021