CF cystic fibrosis


Diagnosis

Treatment

  • cystic fibrosis treat with Trikafta over mono or dual therapy
  • Maybe aztreonam
  • Start azithromycin after 2nd exacerbation
  • Stool elastase for pancreatic insufficency. If low then Creon
  • Once a year labs usually
    • IgE and eos to screen for ABPA
    • CMP for CF related liver and trikafta
    • CBC: for anemia
    • Immunoglobulins: immunodeficiency
    • Can have hyponatremia and Chloride because they can sweat with exercise
  • Supplement with oral NaCl tablets

Complications

Exacerbation

Literature Notes


Maybe aztreonam

Stool elastase for pancreatic insufficency. If low then Creon

Once a year labs usually

Start azithromycin after 2nd exacerbation

IgE and eos to screen for ABPA

CMP for CF related liver and trikafta

CBC: for anemia

Immunoglobulins: immunodeficiency

Can have hyponatremia and Chloride because they can sweat with exercise

Supplement with oral NaCl tablets