CF cystic fibrosis
- related: Pulmonology
- tags: #pulmonology
Diagnosis
Treatment
- cystic fibrosis treat with Trikafta over mono or dual therapy
- Maybe aztreonam
- Start azithromycin after 2nd exacerbation
- Stool elastase for pancreatic insufficency. If low then Creon
- Once a year labs usually
- IgE and eos to screen for ABPA
- CMP for CF related liver and trikafta
- CBC: for anemia
- Immunoglobulins: immunodeficiency
- Can have hyponatremia and Chloride because they can sweat with exercise
- Supplement with oral NaCl tablets
Complications
- CF patients are at increased risks for ABPA: diagnosis of ABPA includes eosinophil count, antibody level, and CT image findings.
- CF patients are at increased risk for NTM MAC infections
Exacerbation
- symptoms of cystic fibrosis exacerbation include appetite loss and decreased FEV1
- treatment of cystic fibrosis exacerbation
Literature Notes
Maybe aztreonam
Stool elastase for pancreatic insufficency. If low then Creon
Once a year labs usually
Start azithromycin after 2nd exacerbation
IgE and eos to screen for ABPA
CMP for CF related liver and trikafta
CBC: for anemia
Immunoglobulins: immunodeficiency
Can have hyponatremia and Chloride because they can sweat with exercise
Supplement with oral NaCl tablets
Links to this note
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CF patients are at increased risk for NTM MAC infections
- related: CF cystic fibrosis
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- related: CF cystic fibrosis
-
- related: CF cystic fibrosis
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cystic fibrosis treat with Trikafta over mono or dual therapy
- related: CF cystic fibrosis
-
symptoms of cystic fibrosis exacerbation include appetite loss and decreased FEV1
- related: CF cystic fibrosis
-
treatment of cystic fibrosis exacerbation
- related: CF cystic fibrosis
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avoid pulmozyme or dornase alfa in non-cystic fibrosis CF bronchiectasis
- related: bronchiectasis chronic bronchiectasis, CF cystic fibrosis