lymphangioleiomyomatosis has cystic lesions with chylous effusions on chest imaging
- related: lymphangioleiomyomatosis LAM
- tags: #permanent #pulmonology
Links to this note
- An Algorithmic Approach to Lung Disease
- lymphangioleiomyomatosis LAM
- chylothorax is elevated TG with low cholesterol
- lymphangioleiomyomatosis LAM is a rare female only disease with cystic lung lesions
- small cysts with very thin walls
- usually diffusely distributed with otherwise normal lung parenchyma1
- small arteries at periphery of cysts indicates perilobular location in relation to lymphatics
- pleural effusion usually can have white appearance and can be chylous (chylothorax is elevated TG with low cholesterol)2
- sometimes can see ground glass opacities from interstitial edema from lymphatic obstruction
- LAM vs PLCH vs LIP vs PBML image, histology, PFT
- LAM has cysts in normal lungs whereas Langerhan has abnormal lungs