lymphangioleiomyomatosis has cystic lesions with chylous effusions on chest imaging

• related: lymphangioleiomyomatosis LAM
• tags: #permanent #pulmonology

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• small cysts with very thin walls
• usually diffusely distributed with otherwise normal lung parenchyma¹
• small arteries at periphery of cysts indicates perilobular location in relation to lymphatics
• pleural effusion usually can have white appearance and can be chylous (chylothorax is elevated TG with low cholesterol)²

• sometimes can see ground glass opacities from interstitial edema from lymphatic obstruction
• LAM vs PLCH vs LIP vs PBML image, histology, PFT
• LAM has cysts in normal lungs whereas Langerhan has abnormal lungs

Links to this note

• An Algorithmic Approach to Lung Disease

  • lymphangioleiomyomatosis has cystic lesions with chylous effusions on chest imaging

• lymphangioleiomyomatosis LAM

  • lymphangioleiomyomatosis has cystic lesions with chylous effusions on chest imaging

• chylothorax is elevated TG with low cholesterol

  • lymphangioleiomyomatosis has cystic lesions with chylous effusions on chest imaging

• lymphangioleiomyomatosis LAM is a rare female only disease with cystic lung lesions

  • lymphangioleiomyomatosis has cystic lesions with chylous effusions on chest imaging

Footnotes

1. Murray and Nadel Ch 97 Lymphangioleiomyomatosis ↩

2. An Algorithmic Approach to Lung Disease ↩